Dhaliwal Kody, Marslender Shannon
Alameda Health System, Oakland, CA, United States.
Radiol Case Rep. 2023 Jan 22;18(3):1358-1363. doi: 10.1016/j.radcr.2022.11.042. eCollection 2023 Mar.
A perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm with distinctive perivascular epithelioid cells that usually demonstrates myomelanocytic differentiation. PEComas can arise in various organs and generally are benign. Uncommonly PEComas have been documented to be malignant with metastasis most frequently to the lung, liver, lymph nodes, and bone. Here, we present the case of a 59-year-old male with a malignant retroperitoneal PEComa with confirmed metastasis to the femur and suspected metastasis to the liver and lung. The purpose of this case study is to present the progression and findings of a metastatic malignant PEComa.
血管周上皮样细胞肿瘤（PEComa）是一种罕见的间叶性肿瘤，具有独特的血管周上皮样细胞，通常表现为肌黑素细胞分化。PEComa可发生于各种器官，一般为良性。罕见情况下，PEComa被记录为恶性，最常转移至肺、肝、淋巴结和骨。在此，我们报告一例59岁男性，患有恶性腹膜后PEComa，已证实转移至股骨，怀疑转移至肝和肺。本病例研究的目的是展示转移性恶性PEComa的病程及发现。
