Cretin Benjamin, Philippi Nathalie, Bousiges Olivier, Blanc Frédéric
Centre Mémoire, de Ressources et de Recherche d'Alsace (Strasbourg-Colmar), Service de Neurologie des Hôpitaux Universitaires de Strasbourg, Pôle Tête et Cou, 1 Avenue Molière, 67200, Strasbourg, France.
Unité de Neuropsychologie, Service de Neurologie et hôpital de jour de Gériatrie, pôle de Gériatrie, Hôpitaux Universitaires de Strasbourg, Strasbourg, France.
J Neurol. 2023 Apr;270(4):2256-2270. doi: 10.1007/s00415-023-11576-7. Epub 2023 Jan 30.
Transient epileptic amnesia (TEA) is a late-onset epilepsy syndrome encompassing transient iterative amnesias and interictal cognitive impairment, two features that overlap with incipient neurodegenerative dementias. We, therefore, examined the yield of CSF amyloid and tau biomarkers in TEA.
In this retrospective study, 127 TEA patients with unremarkable imaging findings were divided into 2 groups, namely, CSF (n = 71) and no-CSF (n = 56). Both were compared for demographics; medical history; baseline neurological, cognitive, and behavioral features; baseline mesial temporal lobe atrophy; and cognitive follow-up at a median of 13 months. CSF samples were examined for amyloid β-42 peptide as well as phospho-tau and total-tau levels.
At baseline, the CSF-TEA group had significantly (p < 0.01) more frequent mild parkinsonism (42.9% vs. 20%) and cognitive concerns (31% vs. 10.7%), a more blunted sense of smell (34.3% vs. 9.4%), a lower baseline MMSE score (27 vs. 28.9), a more frequent amnestic mild cognitive impairment profile (69% vs. 42.6%), and more atrophic hippocampal changes. At follow-up, the CSF-TEA group had significantly (p < 0.01) lower MMSE scores (27.8 vs. 28.9). CSF analyses revealed amyloid and/or tau changes in 27 patients (38%), including an Alzheimer's disease (AD) profile in 17 (24%).
This study shows a good diagnostic value of CSF sampling in a specific population of TEA with characteristics suggestive of incipient degenerative diseases (i.e., red flags). It argues for TEA being the inaugurating feature in some cases of AD. More broadly, our results suggest an etiological heterogeneity in TEA.
短暂性癫痫性遗忘症(TEA)是一种迟发性癫痫综合征,包括短暂性反复遗忘和发作间期认知障碍,这两个特征与早期神经退行性痴呆有重叠。因此,我们研究了TEA患者脑脊液中淀粉样蛋白和tau生物标志物的检出率。
在这项回顾性研究中,127例影像学检查无异常的TEA患者被分为两组,即脑脊液组(n = 71)和无脑脊液组(n = 56)。比较两组的人口统计学特征、病史、基线神经、认知和行为特征、基线内侧颞叶萎缩情况以及中位随访13个月时的认知情况。检测脑脊液样本中的淀粉样β-42肽以及磷酸化tau蛋白和总tau蛋白水平。
在基线时,脑脊液-TEA组轻度帕金森综合征(42.9%对20%)、认知问题(31%对10.7%)、嗅觉减退(34.3%对9.4%)更常见,基线简易精神状态检查表(MMSE)评分更低(27对28.9),遗忘型轻度认知障碍模式更常见(69%对42.6%),海马萎缩变化更多。随访时,脑脊液-TEA组的MMSE评分显著更低(27.8对28.9)(p < 0.01)。脑脊液分析显示27例患者(38%)有淀粉样蛋白和/或tau蛋白变化,其中17例(24%)符合阿尔茨海默病(AD)特征。
本研究表明,在具有早期退行性疾病特征(即警示信号)的特定TEA患者群体中,脑脊液采样具有良好的诊断价值。这表明在某些AD病例中,TEA可能是首发特征。更广泛地说,我们的结果提示TEA存在病因异质性。