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心脏手术后获得性急性免疫性血小板减少症:一例挑战性病例。

Acute acquired immune thrombocytopenia after cardiac surgery: A challenging case.

机构信息

Department of Anesthesia and Intensive Care Medicine, ASUFC "Santa Maria della Misericordia" University Hospital of Udine, Udine, Italy.

Department of Anesthesia and Intensive Care Clinic, ASUFC "Santa Maria della Misericordia" University Hospital of Udine; Department of Medicine, University of Udine, Udine, Italy.

出版信息

Ann Card Anaesth. 2023 Jan-Mar;26(1):90-93. doi: 10.4103/aca.aca_37_21.

DOI:10.4103/aca.aca_37_21
PMID:36722595
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9997465/
Abstract

Thrombocytopenia is a common condition that recognizes an infinite number of possible causes, especially in specific settings like the one covered in this case report: the postoperative period of cardiac surgery. We report a case of an old male with multiple comorbidities who underwent a coronary angioplasty procedure and aortic valve replacement. He showed severe thrombocytopenia in the postoperative days. Differential diagnosis required a big effort, also for the experts in the field. Our goal was to aggressively treat the patient with prednisolone, platelets, and intravenous immunoglobulins to maximize the prognosis. Our patient developed no complications and was discharged successfully.

摘要

血小板减少症是一种常见病症,可能由无数种病因引起,尤其是在心脏手术后等特定环境中。本病例报告就涵盖了这样一种情况:我们报告了一例患有多种合并症的老年男性,他接受了冠状动脉成形术和主动脉瓣置换术。他在术后几天出现严重的血小板减少症。鉴别诊断需要付出巨大的努力,即使是该领域的专家也不例外。我们的目标是通过使用泼尼松龙、血小板和静脉注射免疫球蛋白积极治疗患者,以最大限度地提高预后。我们的患者没有出现并发症,并成功出院。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b09e/9997465/ba58c17b55b3/ACA-26-90-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b09e/9997465/ba58c17b55b3/ACA-26-90-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b09e/9997465/ba58c17b55b3/ACA-26-90-g001.jpg

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本文引用的文献

1
American Society of Hematology 2019 guidelines for immune thrombocytopenia.美国血液学会 2019 年免疫性血小板减少症治疗指南。
Blood Adv. 2019 Dec 10;3(23):3829-3866. doi: 10.1182/bloodadvances.2019000966.
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Updated international consensus report on the investigation and management of primary immune thrombocytopenia.更新的原发性免疫性血小板减少症的调查和管理国际共识报告。
Blood Adv. 2019 Nov 26;3(22):3780-3817. doi: 10.1182/bloodadvances.2019000812.
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Risk factors for bleeding, including platelet count threshold, in newly diagnosed immune thrombocytopenia adults.
新诊断的成人免疫性血小板减少症患者出血的风险因素,包括血小板计数阈值。
J Thromb Haemost. 2018 Sep;16(9):1830-1842. doi: 10.1111/jth.14227. Epub 2018 Aug 12.
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Efficacy and Safety of a New 10% Intravenous Immunoglobulin Product in Patients with Primary Immune Thrombocytopenia (ITP).新型 10%静脉注射免疫球蛋白产品治疗原发免疫性血小板减少症(ITP)患者的疗效和安全性。
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Clinical updates in adult immune thrombocytopenia.成人免疫性血小板减少症的临床进展
Blood. 2017 May 25;129(21):2829-2835. doi: 10.1182/blood-2017-03-754119. Epub 2017 Apr 17.
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The American Society of Hematology 2011 evidence-based practice guideline for immune thrombocytopenia.美国血液学会 2011 年免疫性血小板减少症循证实践指南。
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Pathophysiology and management of chronic immune thrombocytopenia: focusing on what matters.慢性免疫性血小板减少症的病理生理学和治疗:关注要点。
Br J Haematol. 2011 Jan;152(1):52-60. doi: 10.1111/j.1365-2141.2010.08412.x. Epub 2010 Nov 18.
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Hematology. 2009 Aug;14(4):227-36. doi: 10.1179/102453309X439773.
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Standardization of terminology, definitions and outcome criteria in immune thrombocytopenic purpura of adults and children: report from an international working group.成人及儿童免疫性血小板减少性紫癜术语、定义及疗效标准的标准化:国际工作组报告
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10
Changes in platelet count after cardiac surgery can effectively predict the development of pathogenic heparin-dependent antibodies.心脏手术后血小板计数的变化可有效预测致病性肝素依赖性抗体的产生。
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