Pathak Bhavinee, Maimoon Sabiha
Pathology, Narendra Kumar Prasadrao (NKP) Salve Institute of Medical Sciences, Nagpur, IND.
Cureus. 2023 Jan 1;15(1):e33208. doi: 10.7759/cureus.33208. eCollection 2023 Jan.
Dermatofibrosarcoma protuberans is a rare, low-grade dermal soft-tissue tumor with a high propensity for recurrence but a low propensity for metastatic spread. It mostly affects the head, neck, proximal extremities, and trunk. We report a case of dermatofibrosarcoma protuberans over the right lumbar region. The patient presented with swelling in the right lumbar region measuring 3 cm × 3 cm. The local region ultrasonography (USG) revealed a well-defined hypoechoic lesion in the subcutaneous area. The patient was provisionally diagnosed with a peripheral nerve sheath tumor under evaluation. USG-guided fine needle aspiration cytology(FNAC) suggested a spindle cell tumor. Wide local excision of the tumor was performed. Monomorphic spindle cells in a storiform pattern were observed by histological evaluation. The neighboring adipose tissue was invaded by the tumor cells in a honeycomb-shaped pattern. The histological features were suggestive of Dermatofibrosarcoma Protuberans. Due to the high likelihood of recurrence, it is crucial to monitor these patients for an extended period of time.
隆突性皮肤纤维肉瘤是一种罕见的低度真皮软组织肿瘤,复发倾向高但转移扩散倾向低。它主要影响头、颈、近端肢体和躯干。我们报告一例右侧腰部的隆突性皮肤纤维肉瘤病例。患者右侧腰部出现一个3厘米×3厘米的肿胀。局部超声检查(USG)显示皮下区域有一个边界清晰的低回声病变。该患者在评估中被初步诊断为周围神经鞘瘤。超声引导下细针穿刺细胞学检查(FNAC)提示为梭形细胞瘤。对肿瘤进行了广泛局部切除。组织学评估观察到呈席纹状排列的单形性梭形细胞。肿瘤细胞呈蜂窝状侵犯邻近的脂肪组织。组织学特征提示为隆突性皮肤纤维肉瘤。由于复发可能性高,长期监测这些患者至关重要。