De Sousa Machado André, Silva Ana, Silva Jose, Brandão José R, Meireles Luís
Otolaryngology - Head and Neck Surgery, Centro Hospitalar Universitário do Porto, Porto, PRT.
Neuroradiology, Centro Hospitalar Universitário do Porto, Porto, PRT.
Cureus. 2023 Jan 1;15(1):e33206. doi: 10.7759/cureus.33206. eCollection 2023 Jan.
Usually occurring entirely intrasellarly or extending suprasellarly (intra-suprasellar), Rathke's cleft cysts (RCCs) can present with an intrasphenoidal location. Extrasellar positions are rare. To date, only seven patients with intrasphenoidal RCC have been reported in the literature. Despite the rarity of the condition and the lack of pathognomonic radiological features, preoperative diagnosis remains challenging. A trans-sphenoidal approach can be adopted to treat this type of cyst, which has great clinical relevance. Awareness of this different presentation of RCC before respective management may be of value in its approach. Intrasphenoidal RCC should be diagnosed preoperatively and the surgical approach should be changed accordingly by aspiration and partial removal before the histological examination.
拉克氏囊肿(RCCs)通常完全位于鞍内或向鞍上延伸(鞍内-鞍上型),也可表现为蝶窦内位置。鞍外位置罕见。迄今为止,文献中仅报道了7例蝶窦内RCC患者。尽管该病罕见且缺乏特征性的放射学表现,但术前诊断仍具有挑战性。可采用经蝶窦入路治疗此类囊肿,这具有重要的临床意义。在进行相应治疗前,了解RCC的这种不同表现形式可能对治疗方法的选择有帮助。蝶窦内RCC应在术前诊断,并在组织学检查前通过抽吸和部分切除相应改变手术入路。