Thong Y H, Maxwell G M
Aust N Z J Med. 1978 Aug;8(4):436-8. doi: 10.1111/j.1445-5994.1978.tb04920.x.
Selective deficiency of IgM as a primary disorder is seldom encountered1--3, and the syndrome remains ill-defined4. It is generally accepted that for a diagnosis to be made, the serum IgM level should be consistently below 2 SD of normal, no other immunodeficiencies are present, and it is not secondary to other disease processes4. This report of an additional case may provide further insight into this rare disease.
作为一种原发性疾病，选择性IgM缺乏症很少见1 - 3，且该综合征的定义仍不明确4。普遍认为，要做出诊断，血清IgM水平应持续低于正常水平的2个标准差，不存在其他免疫缺陷，且不是继发于其他疾病过程4。这例新增病例的报告可能会为这种罕见疾病提供进一步的见解。
