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误诊为异物吸入的上腔静脉综合征:一例报告

Superior Mediastinal Syndrome Misdiagnosed as Foreign Body Aspiration: A Case Report.

作者信息

Qureshi Tabinda Naz, Beg Mirza Amanullah, Haider Syed Rizwan, Shaaban Naglaa, Abdwani Raghad, Al Rawas Abdulhakim

机构信息

Child Health Department, Sultan Qaboos University Hospital, Muscat, Oman.

Radiology Department, Sultan Qaboos University Hospital, Muscat, Oman.

出版信息

Oman Med J. 2023 Jan 31;38(1):e469. doi: 10.5001/omj.2023.07. eCollection 2023 Jan.

DOI:10.5001/omj.2023.07
PMID:36742180
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9890211/
Abstract

Superior mediastinal syndrome is a life-threatening pediatric oncological emergency that requires high level of awareness and clinical suspicion to avoid misdiagnosis and devastating outcomes. Early diagnostic evaluation and management of underlying etiology are of utmost significance for optimal results. In children, it is most commonly caused by non-Hodgkin's lymphoma and T-cell lymphoblastic leukemia. We report a case of a six-year-old boy with superior mediastinal syndrome secondary to T-cell acute lymphoblastic leukemia, initially misdiagnosed as foreign body aspiration and underwent a procedure with a life-threatening outcome.

摘要

上腔静脉综合征是一种危及生命的儿科肿瘤急症,需要高度的警惕性和临床怀疑,以避免误诊和造成严重后果。对潜在病因进行早期诊断评估和管理对于取得最佳治疗效果至关重要。在儿童中,它最常见的病因是非霍奇金淋巴瘤和T细胞淋巴母细胞白血病。我们报告一例6岁男孩因T细胞急性淋巴细胞白血病继发上腔静脉综合征,最初被误诊为异物吸入,并接受了一次导致生命垂危后果的手术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c15f/9890211/2ead954690a9/OMJ-38-01-2100098-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c15f/9890211/b194e66052a8/OMJ-38-01-2100098-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c15f/9890211/2ead954690a9/OMJ-38-01-2100098-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c15f/9890211/b194e66052a8/OMJ-38-01-2100098-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c15f/9890211/2ead954690a9/OMJ-38-01-2100098-f2.jpg

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本文引用的文献

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Cureus. 2020 Jun 26;12(6):e8838. doi: 10.7759/cureus.8838.
2
Vena cava superior syndrome in the children with mediastinal tumors: Single-center experience.儿童纵隔肿瘤合并上腔静脉综合征:单中心经验
North Clin Istanb. 2020 Apr 9;7(3):255-259. doi: 10.14744/nci.2019.46354. eCollection 2020.
3
Procedural sedation for a child with a mediastinal mass and superior vena caval syndrome.对患有纵隔肿块和上腔静脉综合征的儿童进行程序性镇静。
J Anaesthesiol Clin Pharmacol. 2015 Jul-Sep;31(3):421-4. doi: 10.4103/0970-9185.161735.
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Anesthetic management of patients with anterior mediastinal masses undergoing chamberlain procedure (anterior mediastinostomy).接受张伯伦手术(前纵隔切开术)的前纵隔肿物患者的麻醉管理。
Iran Red Crescent Med J. 2013 Apr;15(4):373-4. doi: 10.5812/ircmj.2120. Epub 2013 Apr 5.
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Superior vena cava syndrome in children.儿童上腔静脉综合征
Indian J Hematol Blood Transfus. 2008 Mar;24(1):28-30. doi: 10.1007/s12288-008-0020-0. Epub 2008 May 1.
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Superior mediastinal syndrome: emergency management.上纵隔综合征:急症处理。
Indian J Pediatr. 2013 Jan;80(1):55-9. doi: 10.1007/s12098-012-0884-8. Epub 2012 Oct 10.
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Anesthetic management of superior vena cava syndrome due to anterior mediastinal mass.前纵隔肿物所致上腔静脉综合征的麻醉管理
J Anaesthesiol Clin Pharmacol. 2012 Apr;28(2):242-6. doi: 10.4103/0970-9185.94910.
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Indian Pediatr. 2011 Jan;48(1):78-9.
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