Choi Soojin, Rhee Seung Yeon, Kim Hyoung Seop
Department of Physical Medicine and Rehabilitation, National Health Insurance Service Ilsan Hospital, Goyang, Korea.
Brain Neurorehabil. 2019 Dec 2;13(2):e8. doi: 10.12786/bn.2020.13.e8. eCollection 2020 Jul.
Chorea hyperglycemia basal ganglia (CHBG) syndrome is an uncommon manifestation of diabetes seen in patients with poor glycemic control. It is characterized by sudden onset of chorea with characteristic hyperintensities of the basal ganglia on brain magnetic resonance imaging. We report a case of a 31-year-old female patient with a history of type 1 diabetes mellitus, renal failure, and hypertension, who presented with acute symptoms of chorea involving both the upper and lower limbs with facial and cervical dystonia. Magnetic resonance imaging revealed bilateral hyperintensities of the globus pallidus and putamen. Control of blood glucose levels led to resolution of the choreic movements. In addition, follow-up magnetic resonance imaging studies revealed improvement in the hyperintensities of the basal ganglia bilaterally.
舞蹈症-高血糖-基底节(CHBG)综合征是血糖控制不佳的糖尿病患者中一种不常见的表现形式。其特征为突然出现舞蹈症,且脑部磁共振成像显示基底节有特征性高信号。我们报告一例31岁女性患者,有1型糖尿病、肾衰竭和高血压病史,出现累及上下肢的急性舞蹈症症状,并伴有面部和颈部肌张力障碍。磁共振成像显示双侧苍白球和壳核高信号。血糖水平的控制使舞蹈样动作得以缓解。此外,后续的磁共振成像研究显示双侧基底节高信号有所改善。