Department of Hematology, Tohoku University Hospital, 1-1, Seiryo-Machi, Aoba-Ku, Sendai, Miyagi, 980-8574, Japan.
Department of Hematology, Miyagi Cancer Center, Miyagi, Japan.
Int J Hematol. 2023 May;117(5):738-747. doi: 10.1007/s12185-023-03546-6. Epub 2023 Feb 9.
Early T-cell precursor (ETP) acute lymphoblastic leukemia/lymphoma (ALL) is generally considered to be a high-risk subtype. We retrospectively analyzed the clinical outcomes of adult patients diagnosed with ETP-ALL or other T-cell ALL (non-ETP T-ALL). The subjects were 82 patients (ETP-ALL: n = 18, non-ETP T-ALL: n = 64) for whom relevant immunophenotype data needed for classification were available. ETP-ALL patients were older (median age, 50.5 vs. 33.5 years, P = 0.042) and had less mediastinal involvement (27.8 vs. 73.4%, P < 0.001). The rate of complete remission (CR) with the first induction therapy was significantly lower in the ETP group (33.3 vs. 64.0%, P = 0.03), but the CR rate within 2 cycles of chemotherapy did not differ significantly (61.1 vs. 76.6%, P = 0.232). The 3-year overall survival (OS) rate was also similar in both groups (43.2 vs. 45.8%, P = 0.992). The ETP phenotype had no impact on survival in the transplant group or the non-transplant group. A multivariate analysis identified the male sex as a poor prognostic factor (HR: 4.43, P < 0.01), but not the immunophenotype of ETP. The prognosis for adult patients with ETP-ALL was comparable to that of non-ETP T-ALL patients. However, further studies aimed at improving the remission rate for ETP-ALL are needed.
早期 T 细胞前体(ETP)急性淋巴细胞白血病/淋巴瘤(ALL)通常被认为是一种高风险亚型。我们回顾性分析了诊断为 ETP-ALL 或其他 T 细胞 ALL(非 ETP T-ALL)的成年患者的临床结局。这些患者为 82 例(ETP-ALL:n=18,非 ETP T-ALL:n=64),他们具有分类所需的相关免疫表型数据。ETP-ALL 患者年龄较大(中位年龄 50.5 岁 vs. 33.5 岁,P=0.042),纵隔受累较少(27.8% vs. 73.4%,P<0.001)。首次诱导治疗的完全缓解(CR)率在 ETP 组明显较低(33.3% vs. 64.0%,P=0.03),但化疗 2 个周期内的 CR 率无显著差异(61.1% vs. 76.6%,P=0.232)。两组的 3 年总生存(OS)率也相似(43.2% vs. 45.8%,P=0.992)。ETP 表型在移植组或非移植组中对生存均无影响。多因素分析确定男性为不良预后因素(HR:4.43,P<0.01),但 ETP 的免疫表型不是。成年 ETP-ALL 患者的预后与非 ETP T-ALL 患者相当。然而,需要进一步的研究来提高 ETP-ALL 的缓解率。