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病例 311:全身性淋巴异常。

Case 311: Generalized Lymphatic Anomaly.

机构信息

From the Department of Body Imaging, Centro Radiológico Dr. Luis Méndez Collado, Muñecas 444, San Miguel de Tucumán, Tucumán, Argentina T4000.

出版信息

Radiology. 2023 Mar;306(3):e213229. doi: 10.1148/radiol.213229.

DOI:10.1148/radiol.213229
PMID:36803000
Abstract

A 14-year-old boy presented with asthenia, low back pain, and abdominal distention. The onset of symptoms was slow and progressive over a few months. The patient had no contributing past medical history. At physical examination, all vital signs were normal. Only pallor and positive fluid wave test results were noted; there was no lower limb edema, mucocutaneous lesions, or palpable lymph node enlargement. Laboratory work-up revealed a decreased hemoglobin concentration of 9.3 g/dL (normal range, 12-16 g/dL) and a decreased hematocrit level of 29.8% (normal range, 37%-45%), but all other laboratory values were normal. Contrast-enhanced CT of the chest, abdomen, and pelvis was performed.

摘要

一位 14 岁男孩因乏力、腰痛和腹胀就诊。症状开始缓慢且逐渐加重,历时数月。患者无其他既往病史。体格检查时,所有生命体征均正常。仅发现面色苍白和阳性液波震颤征;下肢无水肿、黏膜皮肤病变或可触及的淋巴结肿大。实验室检查发现血红蛋白浓度为 9.3g/dL(正常范围 12-16g/dL),血细胞比容水平为 29.8%(正常范围 37%-45%)下降,但其他实验室值均正常。进行了胸部、腹部和骨盆的增强 CT 检查。

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