Owada Yoshiyuki, Tachibana Takaaki, Tokuhara Kaori, Ikeda Taro, Hosono Masayoshi, Okazaki Taro, Ienaga Tetsuya, Ikura Yoshihiro, Iwai Yasuhiro
Dept. of Gastroenterological Surgery, Takatsuki General Hospital.
Gan To Kagaku Ryoho. 2023 Feb;50(2):261-263.
A 56-year-old man with diarrhea and bloody stools was found to have a type 2 tumor in the rectosigmoid region. A biopsy revealed well-differentiated tubular adenocarcinoma(tub1), and laparoscopic high anterior resection was performed. The final diagnosis was MiNEN(NEC:adenocarcinoma=6:4), RS, type 2, Ly0, V0, pT3(SS), pN0, M0, and pStage Ⅱa. He has been followed up without postoperative adjuvant chemotherapy and has been alive without recurrence for 1 year and 4 months after surgery. MiNEN is a rare disease, and most of them are mixed with NEC components or high- grade NET G3 and have a poor prognosis. We present an important case of rectal MiNEN.
一名56岁腹泻伴便血的男性患者被发现直肠乙状结肠区域有2型肿瘤。活检显示为高分化管状腺癌(tub1),遂行腹腔镜高位前切除术。最终诊断为MiNEN(神经内分泌癌:腺癌=6:4),RS,2型,Ly0,V0,pT3(SS),pN0,M0,pⅡa期。术后未进行辅助化疗,对其进行随访,术后1年4个月仍存活且无复发。MiNEN是一种罕见疾病,大多数病例合并神经内分泌癌成分或高级别NET G3,预后较差。我们报告一例直肠MiNEN的重要病例。