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一名年轻女性的原发性皮肤CD4 +小/中型多形性T细胞淋巴增殖性疾病

Primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoproliferative disorder in a young woman.

作者信息

Leeolou Melissa C, Young Peter A, Saleem Atif, Narala Saisindhu, Bae Gordon H

机构信息

Department of Dermatology, Stanford University School of Medicine, Stanford, California, USA.

出版信息

Dermatol Online J. 2022 Dec 15;28(6). doi: 10.5070/D328659726.

DOI:10.5070/D328659726
PMID:36809093
Abstract

Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (CD4+PCSM-LPD) is a low-grade cutaneous T cell disorder. There is no standardized approach to treatment of CD4+ PCSM-LPD due to its rarity. Herein, we discuss a 33-year-old woman with CD4+PCSM-LPD which resolved after a partial biopsy. We highlight that conservative and local treatment modalities should be considered prior to utilizing more aggressive and invasive treatment options.

摘要

原发性皮肤CD4+小/中型T细胞淋巴增殖性疾病(CD4+PCSM-LPD)是一种低度皮肤T细胞疾病。由于其罕见性,目前尚无针对CD4+PCSM-LPD的标准化治疗方法。在此,我们讨论一名33岁患有CD4+PCSM-LPD的女性患者,其在部分活检后病情缓解。我们强调,在采用更积极和侵入性的治疗方案之前,应考虑保守和局部治疗方式。

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