Cremin B J, Viljoen D L, Wynchank S, Beighton P
Department of Paediatric Radiology, Red Cross Children's Hospital, Rondebosch, South Africa.
Pediatr Radiol. 1987;17(6):486-8. doi: 10.1007/BF02388284.
The Proteus syndrome is a recently delineated group of skeletal and mesodermal malformations. Its characteristics include hemihypertrophy and fatty/lymphangiomatous masses. This description outlines the imaging sequences available to the radiologist. It is mainly concerned with the use of magnetic resonance imaging. This shows the extent of the mesodermal malformation with particular reference to the extent of intra abdominal infiltration.
变形综合征是一组最近才被描述的骨骼和中胚层畸形。其特征包括半身肥大以及脂肪/淋巴管瘤性肿块。本描述概述了放射科医生可用的成像序列。主要涉及磁共振成像的应用。这显示了中胚层畸形的范围,尤其涉及腹腔内浸润的范围。