Department of Pediatric Surgery, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Sultan Qaboos Univ Med J. 2023 Feb;23(1):119-121. doi: 10.18295/squmj.9.2021.138. Epub 2023 Feb 23.
Duplication of urethra is a rare congenital anomaly; a Y-shaped urethral duplication is the rarest variant and lacks a standardised treatment plan. We report a nine-year-old male patient with a Y-duplication of urethra diagnosed during neonatal age who presented to a tertiary care teaching hospital in India in 2018. The patient had undergone a vesicostomy on the seventh day of life for passing urine per anus and was lost to follow-up thereafter. At eight years of age, there was a failed attempt at disconnection of the duplicated urethral tract from the anus after colostomy. The patient was managed successfully by progressive dilatation of the orthotopic urethra, which required multiple stages, followed by separation of the urethra from the rectum. At three-years follow-up the patient was continent and asymptomatic.
尿道重复畸形是一种罕见的先天性异常；Y 型尿道重复畸形是最罕见的一种变异，缺乏标准化的治疗方案。我们报告了一名 9 岁男性患者，他在新生儿期被诊断为 Y 型尿道重复畸形，于 2018 年在印度一家三级教学医院就诊。该患者在出生后第 7 天因经肛门排尿而接受了膀胱造口术，此后失访。8 岁时，在结肠造口术失败后，尝试从肛门分离重复的尿道。通过多次阶段性的原位尿道扩张，成功地对患者进行了治疗，随后将尿道与直肠分离。在 3 年的随访中，患者有控制能力，无症状。
