Catalano Marco, Crimi Luca, Galioto Federica, Coronella Maria, Foti Pietro Valerio, Palmucci Stefano, Basile Antonio
Department of Medical Surgical Sciences and Advanced Technologies "GF Ingrassia", Radiology Unit 1, University Hospital Policlinico "G. Rodolico-San Marco", Catania, 95123, Italy.
Respir Med Case Rep. 2023 Feb 19;42:101822. doi: 10.1016/j.rmcr.2023.101822. eCollection 2023.
Pulmonary artery intimal sarcoma (PAIS) is a rare malignant neoplasm with imaging features that can mimic pulmonary embolism (PE). It must be recognized early because a radical resection may be useful to prolong survival.
A clinical case of a 57-year-old Caucasian male affected by PAIS is presented, which describes the computed tomography (CT) findings found in PAIS and the elements of overlap and differentiation with PE. The main common element is represented by the endoluminal filling defect of the pulmonary arterial vessels in contrast-enhanced CT examinations; a characteristic polypoid morphology or polylobulated contours are typical findings of PAIS. Other specific elements of the neoplasm such as wall eclipse sign, extension beyond the arterial wall, and metastasis are also explained.
The overlap of the clinical-radiological findings and the epidemiological difference between PAIS and PE cause a diagnostic delay. By knowing the differential elements, the radiologist can detect the neoplasm early to accelerate diagnosis and suggest optimal management.
肺动脉内膜肉瘤（PAIS）是一种罕见的恶性肿瘤，其影像学特征可模拟肺栓塞（PE）。必须尽早识别，因为根治性切除可能有助于延长生存期。
本文介绍了一名57岁患有PAIS的白种男性的临床病例，描述了PAIS的计算机断层扫描（CT）表现以及与PE的重叠和鉴别要点。主要的共同特征是增强CT检查中肺动脉血管的腔内充盈缺损；息肉样形态或分叶状轮廓是PAIS的典型表现。还解释了该肿瘤的其他特定特征，如管壁缺损征、超出动脉壁的延伸以及转移。
PAIS与PE的临床放射学表现重叠以及流行病学差异导致诊断延迟。通过了解鉴别要点，放射科医生可以早期发现肿瘤，加速诊断并建议最佳治疗方案。
