Arora Nikhil, Kumar Pratik, Goel Ashiya
Department of Otorhinolaryngology, Pt B. D. Sharma PGIMS, Rohtak, Haryana, India.
Ann Maxillofac Surg. 2022 Jul-Dec;12(2):212-215. doi: 10.4103/ams.ams_22_22. Epub 2022 Dec 16.
Biphenotypic sinonasal sarcoma is a rare malignant tumour exclusively involving the sinonasal cavity. These tumours have variable and atypical presentations. Early approach and correct treatment modalities are key factors in the management of such cases.
A 48-year-old male patient presented with left-sided nasal obstruction and intermittent nasal bleeding for one year.
Biphenotypic sinonasal sarcoma confirmed on histopathological examination and immunohistochemistry.
The patient underwent surgical excision with left lateral rhinotomy and bifrontal craniotomy with skull base repair. The patient also received postoperative radiotherapy.
The patient is on regular follow-up with no similar complaints.
TAKE-AWAY LESSON: Treating team should keep the diagnosis of biphenotypic sinonasal sarcoma in mind while investigating a patient with nasal mass. Surgical management is the treatment of choice, due to its local aggressive nature and proximity to the brain and eyes. Postoperative radiotherapy is vital to prevent tumour recurrence.
双表型鼻窦肉瘤是一种罕见的恶性肿瘤，仅累及鼻窦腔。这些肿瘤表现多样且不典型。早期诊断和正确的治疗方式是处理此类病例的关键因素。
一名48岁男性患者出现左侧鼻塞和间歇性鼻出血1年。
经组织病理学检查和免疫组化确诊为双表型鼻窦肉瘤。
患者接受了左侧鼻侧切开术和双额开颅术加颅底修复的手术切除。患者还接受了术后放疗。
患者定期随访，无类似主诉。
在对有鼻腔肿物的患者进行检查时，治疗团队应考虑到双表型鼻窦肉瘤的诊断。由于其局部侵袭性以及与脑和眼的毗邻关系，手术治疗是首选治疗方法。术后放疗对于预防肿瘤复发至关重要。
