Department of Neurology, Albert Szent-Györgyi Clinical Center, University of Szeged, Szeged.
Department of Radiology, Albert Szent-Györgyi Clinical Center, University of Szeged, Szeged.
Ideggyogy Sz. 2023 Jan 30;76(1-2):58-62. doi: 10.18071/isz.76.0058.
IgG4-related (IgG4-RD) disease is a relatively newly identified, chronic autoimmune disorder that can affect any organ system. The disease is relatively rare. It has mostly systemic presentation, however it can also appear in isolated form in one single organ. In our report, we demonstrate an elderly male patient’s case with IgG4-RD presented in the form of diffuse meningeal inflammation and hypertrophic pachymeningitis with one-sided cranial nerve and intraventricular involvement.
IgG4 相关疾病（IgG4-RD）是一种新近确定的慢性自身免疫性疾病，可影响任何器官系统。该疾病较为罕见，多为全身性表现，但也可单独累及单一器官。在本报告中，我们展示了一位老年男性 IgG4-RD 患者的病例，其表现为弥漫性脑膜炎症和肥厚性硬脑膜炎，伴有单侧颅神经和脑室受累。
