一名3岁儿童的支气管内炎性肌纤维母细胞瘤

Endobronchial Inflammatory Myofibroblastic Tumor in a 3-Year-Old Child.

作者信息

Guanà Riccardo, Carpino Andrea, Miglietta Marta, Zambaiti Elisa, Cerrina Alessia, Lonati Luca, Guerrera Francesco, Vallero Stefano, Garofalo Salvatore, Bardessono Marco, Maletta Francesca, Shilly Steffi, Gennari Fabrizio

机构信息

Division of Pediatric General, Thoracic & Minimally Invasive Surgery, University Hospital of Health and Science, Turin University, Regina Margherita Children's Hospital, Torino, Italy.

Columbia University School of Nursing, New York, New York, United States.

出版信息

European J Pediatr Surg Rep. 2023 Mar 9;11(1):e5-e9. doi: 10.1055/s-0043-1764289. eCollection 2023 Jan.

DOI:10.1055/s-0043-1764289

PMID:36911852

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10019996/

Abstract

Inflammatory myofibroblastic tumor (IMT) is a mesenchymal tumor that can occur at any age. However, it is primarily seen in children, with the most common site being in the lung parenchyma, usually present with rare endobronchial lesions. This case reports the incidence in a 3-year-old girl diagnosed with pericardiac pneumonia treated with antibiotics with no clinical improvement. A chest computed tomography (CT) scan identified a 1.5-cm lesion in the left main bronchus. Bronchoscopy revealed complete obstruction of the left main stem bronchus. A left posterolateral thoracotomy was performed. Additionally, a left sleeve upper bronchial resection was conducted under fibroendoscopic control. Definitive histology confirmed IMT. After 2 years of endoscopic follow-up, there is no evidence of recurrence.

摘要

炎性肌纤维母细胞瘤（IMT）是一种可发生于任何年龄的间叶性肿瘤。然而，它主要见于儿童，最常见的部位是肺实质，通常表现为罕见的支气管内病变。本病例报告了一名3岁女孩的发病情况，该女孩被诊断为心包肺炎，使用抗生素治疗后临床症状无改善。胸部计算机断层扫描（CT）显示左主支气管有一个1.5厘米的病变。支气管镜检查显示左主支气管完全阻塞。进行了左后外侧开胸手术。此外，在纤维内镜控制下进行了左袖状上叶支气管切除术。最终组织学检查确诊为IMT。经过2年的内镜随访，没有复发的迹象。