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成功分娩一名患有室间隔缺损并伴有艾森曼格综合征的女性:病例报告。

Successful delivery in a woman with ventricular septal defect complicated with Eisenmenger syndrome: case report.

机构信息

Cadi Ayyad University, Faculty of Medicine and Pharmacy of Marrakesh, Marrakesh, Morrocco.

出版信息

Pan Afr Med J. 2022 Dec 9;43:188. doi: 10.11604/pamj.2022.43.188.32982. eCollection 2022.

DOI:10.11604/pamj.2022.43.188.32982
PMID:36915419
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10007704/
Abstract

Eisenmenger syndrome is a dramatic complication of certain heart diseases. It is an absolute contra-indication to pregnancy because it holds a high risk of maternal-fetal mortality. Nowadays, we don´t see much of this condition, because congenital heart defects are diagnosed during childhood, infancy, or prenatally; and even if a pregnancy occurs, it is usually terminated as soon as it is diagnosed. Nevertheless, some women are willing to carry the risks that come with their condition. We report the case of a 26-year-old woman with an undiagnosed interventricular septal wall defect that evolved into Eisenmenger syndrome during her pregnancy. A successful elective C-section was done under epidural anesthesia and close monitoring. When facing this challenging situation, there are no clear guidelines, however, premature and elective delivery is paramount.

摘要

艾森曼格综合征是某些心脏病的严重并发症。它是妊娠的绝对禁忌证,因为它有很高的母婴死亡率。如今,我们很少见到这种情况,因为先天性心脏病在儿童期、婴儿期或产前就能被诊断出来;即使发生妊娠,一旦被诊断出来通常也会终止。然而,有些女性愿意承担伴随病情而来的风险。我们报告了一例 26 岁的女性,她患有未被诊断的室间隔壁缺损,在妊娠期间发展为艾森曼格综合征。在硬膜外麻醉和密切监测下成功进行了选择性剖宫产。当面对这种具有挑战性的情况时,没有明确的指南,但早产和选择性分娩至关重要。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b4c6/10007704/956c9a3ad382/PAMJ-43-188-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b4c6/10007704/60e1538b90a8/PAMJ-43-188-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b4c6/10007704/956c9a3ad382/PAMJ-43-188-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b4c6/10007704/60e1538b90a8/PAMJ-43-188-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b4c6/10007704/956c9a3ad382/PAMJ-43-188-g002.jpg

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本文引用的文献

1
Eisenmenger Syndrome and Pregnancy: Novel ECMO Configuration as a Bridge to Delivery and Recovery Utilizing a Multidisciplinary Team.艾森曼格综合征与妊娠:利用多学科团队,采用新型体外膜肺氧合配置作为分娩和康复的桥梁
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Therapeutic methods used in patients with Eisenmenger syndrome.艾森曼格综合征患者的治疗方法。
Cardiol J. 2009;16(6):500-6.
8
Has there been any progress made on pregnancy outcomes among women with pulmonary arterial hypertension?肺动脉高压女性的妊娠结局有什么进展吗?
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