Department of Surgery, King Edward Medical University, Mayo Hospital,Lahore, Pakistan.
Department of Surgery, King Edward Medical University, Mayo Hospital, Lahore, Pakistan.
J Pak Med Assoc. 2023 Mar;73(3):677-680. doi: 10.47391/JPMA.5245.
Choledochal Cyst (CC), also known as the biliary cyst, is one of the rare inherited anomalies of intrahepatic and/or extrahepatic biliary system characterised by varying degrees of cystic dilatation of the biliary tract without acute obstruction. The prevalence ranges from 1 in 13,000 people to 1 in 2 million people with preponderance in Asia1, particularly in Japan. Moreover, the presentation also varies in children and adults, and is usually vaguer and non-specific in adults. The prevalence is even lower in males, with female to male ratio being 3:1-4:12. We present here three cases of adult choledochal cysts excised in our surgical unit in the last five years. We discuss the aetiopathogenesis, presentation, diagnosis, surgical treatment, and complications of choledochal cysts based on the available literature. It is crucial to establish a multidisciplinary group of professionals, that comprises paediatric surgeons, pathologists, paediatric gastroenterologists, physiotherapists, nutritionists, oncologists, and radiologists, to get acceptable outcomes in diagnosing and treating children with choledochal cysts.
胆总管囊肿(CC),又称胆管囊肿,是一种罕见的肝内外胆管先天性异常,其特征为胆管不同程度的囊性扩张,无急性梗阻。其患病率为每 13000 人中有 1 例至每 200 万人中有 1 例,亚洲多见,尤其在日本。此外,儿童和成人的表现也不同,且在成人中通常更模糊、不典型。男性患病率更低,男女比例为 3:1-4:12。我们在此介绍了过去五年中在我们外科病房切除的三例成人胆总管囊肿。我们根据现有文献讨论了胆总管囊肿的病因、发病机制、临床表现、诊断、手术治疗和并发症。建立一个由小儿外科医生、病理学家、小儿胃肠病学家、物理治疗师、营养师、肿瘤学家和放射科医生组成的多学科专业团队至关重要,以获得对患有胆总管囊肿的儿童进行诊断和治疗的可接受结果。