• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

我的做法：用于“揭示”和治疗先天性心脏病中先天性门体静脉连接的新技术。

How I do it: Novel technique to "Unmask" and treat congenital portosystemic venous connections in congenital heart disease.

作者信息

Batlivala Sarosh P, McGovern Eiméar, Goldstein Bryan H

机构信息

Department of Pediatrics, The Heart Institute, Cincinnati Children's Hospital Medical Center, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Department of Pediatrics, University of Kentucky Health Care and Kentucky Children's Hospital, Lexington, KY, USA.

出版信息

Ann Pediatr Cardiol. 2022 Jul-Aug;15(4):394-398. doi: 10.4103/apc.apc_34_22. Epub 2023 Jan 6.

DOI:10.4103/apc.apc_34_22
PMID:36935837
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10015395/
Abstract

Congenital portosystemic venous connections are rare vascular anomalies that connect the portal and systemic venous circulations. These vascular lesions can lead to complex and varied physiologic manifestations in single-ventricle patients as they progress through the various stages of palliation in the Fontan pathway. Specifically, these connections may be unmasked after a superior cavopulmonary anastomosis operation, but then "re-masked" after Fontan completion. We describe the complex physiology with an illustrative case report and present a novel method to unmask these pathologic connections after Fontan completion to facilitate transcatheter occlusion and resolve downstream symptoms.

摘要

先天性门体静脉连接是一种罕见的血管异常，它连接门静脉和体静脉循环。这些血管病变在单心室患者沿着Fontan路径进行各个阶段的姑息治疗过程中，会导致复杂多样的生理表现。具体而言，这些连接可能在进行上腔静脉-肺动脉吻合术后显现出来，但在Fontan手术完成后又会“重新隐匿”。我们通过一个病例报告来说明这种复杂的生理情况，并提出一种新方法，在Fontan手术完成后揭示这些病理性连接，以便于经导管封堵并解决下游症状。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/0082b65b9e77/APC-15-394-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/4b6a5becfed2/APC-15-394-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/20c8443d212c/APC-15-394-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/33f12a3b3b12/APC-15-394-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/b7a2e7bcd1f2/APC-15-394-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/af789324f9aa/APC-15-394-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/09814b94389c/APC-15-394-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/0082b65b9e77/APC-15-394-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/4b6a5becfed2/APC-15-394-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/20c8443d212c/APC-15-394-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/33f12a3b3b12/APC-15-394-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/b7a2e7bcd1f2/APC-15-394-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/af789324f9aa/APC-15-394-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/09814b94389c/APC-15-394-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3710/10015395/0082b65b9e77/APC-15-394-g007.jpg

相似文献

1
How I do it: Novel technique to "Unmask" and treat congenital portosystemic venous connections in congenital heart disease.我的做法：用于“揭示”和治疗先天性心脏病中先天性门体静脉连接的新技术。
Ann Pediatr Cardiol. 2022 Jul-Aug;15(4):394-398. doi: 10.4103/apc.apc_34_22. Epub 2023 Jan 6.
2
Novel use of covered stents to treat profound cyanosis in a hepatic vein exclusion Fontan.覆膜支架在肝静脉离断式Fontan手术中治疗重度紫绀的新应用。
Ann Pediatr Cardiol. 2019 Jan-Apr;12(1):60-63. doi: 10.4103/apc.APC_125_18.
3
[Pulmonary ventricle bypass operations].[肺动脉心室旁路手术]
Rev Port Cir Cardiotorac Vasc. 2006 Apr-Jun;13(2):69-74.
4
Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: a case series and literature review.多脾综合征和功能性单心室心脏病患者的先天性门体静脉连接及其他腹部静脉异常：病例系列报道与文献综述
Congenit Heart Dis. 2011 Jan-Feb;6(1):28-40. doi: 10.1111/j.1747-0803.2010.00478.x.
5
Cavopulmonary pathway modification in patients with heterotaxy and newly diagnosed or persistent pulmonary arteriovenous malformations after a modified Fontan operation.腔静脉-肺动脉连接途径改建术治疗非均型房室连接和改良 Fontan 术后新发或持续肺动静脉畸形
J Thorac Cardiovasc Surg. 2011 Jun;141(6):1362-70.e1. doi: 10.1016/j.jtcvs.2010.08.088. Epub 2010 Dec 13.
6
Improved management of systemic venous anomalies in a single ventricle: New rationale.单心室中系统性静脉异常的管理改进：新的理论依据。
J Thorac Cardiovasc Surg. 2009 Nov;138(5):1154-9. doi: 10.1016/j.jtcvs.2009.04.039. Epub 2009 Jul 10.
7
Modification of hemi-Fontan operation for patients with functional single ventricle and anomalous pulmonary venous connection to the superior vena cava: mid-term results.功能性单心室合并肺静脉异常连接至上腔静脉患者的半Fontan手术改良：中期结果
Interact Cardiovasc Thorac Surg. 2016 May;22(5):546-52. doi: 10.1093/icvts/ivv398. Epub 2016 Feb 8.
8
The Bilateral Bidirectional Glenn Operation as a Risk Factor Prior to Fontan Completion in Complex Congenital Heart Disease Patients.双侧双向格林手术作为复杂先天性心脏病患者在完成Fontan手术前的一个危险因素。
World J Pediatr Congenit Heart Surg. 2019 Mar;10(2):174-181. doi: 10.1177/2150135118819997.
9
Anatomical Repair Conversion After Bidirectional Cavopulmonary Shunt for Complex Cardiac Anomalies: Palliation is Not a One-Way Path.复杂心脏畸形双向腔肺分流术后的解剖修复转换：姑息治疗并非单行道。
Pediatr Cardiol. 2018 Mar;39(3):604-609. doi: 10.1007/s00246-017-1800-9. Epub 2018 Jan 3.
10
Congenital Portosystemic Shunt Presenting As Hyperammonemia Following Fontan Operation.Fontan手术后表现为高氨血症的先天性门体分流
JPGN Rep. 2023 Feb 1;4(1):e282. doi: 10.1097/PG9.0000000000000282. eCollection 2023 Feb.

本文引用的文献

1
In Search of "Hepatic Factor": Lack of Evidence for ALK1 Ligands BMP9 and BMP10.寻找“肝脏因子”：缺乏ALK1配体BMP9和BMP10的证据
Am J Respir Crit Care Med. 2021 Jan 15;203(2):249-251. doi: 10.1164/rccm.202005-1937LE.
2
Abernethy malformation: Our experience from a tertiary cardiac care center and review of literature.阿伯内西畸形：我们在三级心脏护理中心的经验及文献综述。
Ann Pediatr Cardiol. 2019 Sep-Dec;12(3):240-247. doi: 10.4103/apc.APC_185_18.
3
Spontaneous closure of arterio-venous pulmonary fistulas by redirection of hepatic venous blood 9 years after Glenn anastomosis in a 12-year-old girl.
Cardiol Young. 2019 Oct;29(10):1287-1289. doi: 10.1017/S1047951119000465.
4
Account of Two Instances of Uncommon Formation in the Viscera of the Human Body: From the Philosophical Transactions of the Royal Society of London.人体内脏罕见构造的两个实例记述：源自《伦敦皇家学会哲学学报》
Med Facts Obs. 1797;7:100-108.
5
Clinical outcomes of early scheduled Fontan completion following Kawashima operation.川岛手术后早期计划性Fontan手术完成的临床结果
Gen Thorac Cardiovasc Surg. 2017 Dec;65(12):692-697. doi: 10.1007/s11748-017-0812-y. Epub 2017 Sep 7.
6
Clinical features of congenital portosystemic shunt in children.儿童先天性门体分流的临床特征。
Eur J Pediatr. 2012 Feb;171(2):395-400. doi: 10.1007/s00431-011-1564-9. Epub 2011 Sep 13.
7
Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: a case series and literature review.多脾综合征和功能性单心室心脏病患者的先天性门体静脉连接及其他腹部静脉异常：病例系列报道与文献综述
Congenit Heart Dis. 2011 Jan-Feb;6(1):28-40. doi: 10.1111/j.1747-0803.2010.00478.x.
8
Hepatic venous blood and the development of pulmonary arteriovenous malformations in congenital heart disease.先天性心脏病中肝静脉血与肺动静脉畸形的发展
Circulation. 1995 Sep 1;92(5):1217-22. doi: 10.1161/01.cir.92.5.1217.