Batlivala Sarosh P, Ebeid Makram R
Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
University of Mississippi Medical Center, Jackson, Mississippi, USA.
Ann Pediatr Cardiol. 2019 Jan-Apr;12(1):60-63. doi: 10.4103/apc.APC_125_18.
Fontan completion in patients with complex cardiac anatomy, and specifically heterotaxy syndrome, can present unique physiologic considerations. For example, existing venous connections may be "unmasked" after a cavopulmonary anastomosis operation. We present the case of a child with heterotaxy, dextrocardia, single-ventricle physiology, and anomalous hepatic venous drainage that resulted in profound shunting and cyanosis. We addressed the problem utilizing a novel strategy with a "fenestrated" covered stent.
对于具有复杂心脏解剖结构，特别是内脏异位综合征的患者，完成Fontan手术可能会带来独特的生理方面的考量。例如，在腔肺吻合手术后，现有的静脉连接可能会“暴露”出来。我们报告了一例患有内脏异位、右位心、单心室生理以及异常肝静脉引流导致严重分流和发绀的儿童病例。我们采用一种使用“开窗”覆膜支架的新策略解决了这个问题。
