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一名36周新生儿的回肠闭锁与全结肠先天性巨结肠症:病例报告

Ileal atresia and total colonic hirschsprung disease in a 36-week neonate: A case report.

作者信息

Atqiaee Khashahyar, Hiradfar Mehran, Mashhadi Mahdi Parvizi, Khanghah Ali Samady

机构信息

Department of Pediatric Surgery, Faculty of Medicine Mashhad University of Medical Sciences Mashhad Iran.

Department of Surgery Ardabil University of Medical Sciences Ardabil Iran.

出版信息

Clin Case Rep. 2023 Mar 14;11(3):e7079. doi: 10.1002/ccr3.7079. eCollection 2023 Mar.

DOI:10.1002/ccr3.7079
PMID:36937634
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10014510/
Abstract

Intestinal atresia and hirschsprung disease are two common causes of bowel obstruction in neonates; simultaneous occurrence is rare. This report delineates a 36-week newborn with ileal atresia and total colonic hirschsprung who was referred to our unit due to failure of meconium passage during the first 48 h after birth.

摘要

肠闭锁和先天性巨结肠是新生儿肠梗阻的两个常见原因;同时发生的情况很少见。本报告描述了一名36周的新生儿,患有回肠闭锁和全结肠先天性巨结肠,因出生后48小时内胎粪未排出而转诊至我院。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/76dceeb38c0e/CCR3-11-e7079-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/cc897ef56563/CCR3-11-e7079-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/76bfdff98fef/CCR3-11-e7079-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/b39ee4ae4d02/CCR3-11-e7079-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/76dceeb38c0e/CCR3-11-e7079-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/cc897ef56563/CCR3-11-e7079-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/76bfdff98fef/CCR3-11-e7079-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/b39ee4ae4d02/CCR3-11-e7079-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a8dd/10014510/76dceeb38c0e/CCR3-11-e7079-g001.jpg

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本文引用的文献

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Int J Surg Case Rep. 2020;74:226-229. doi: 10.1016/j.ijscr.2020.08.023. Epub 2020 Aug 29.
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Hirschsprung Disease - Current Diagnosis and Management.先天性巨结肠症——当前的诊断与管理。
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Pediatric intestinal motility disorders.小儿肠道动力障碍
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Comprehensive review of procedures for total colonic aganglionosis.全结肠无神经节症手术的综合综述
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Enteric nervous system development and Hirschsprung's disease: advances in genetic and stem cell studies.肠道神经系统发育与先天性巨结肠病:遗传和干细胞研究进展
Nat Rev Neurosci. 2007 Jun;8(6):466-79. doi: 10.1038/nrn2137.
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Ileal atresia associated with Hirschsprung disease (total colonic aganglionosis).回肠闭锁合并先天性巨结肠(全结肠无神经节症)。
J Pediatr Surg. 2005 Sep;40(9):e5-7. doi: 10.1016/j.jpedsurg.2005.05.064.
7
Association of colonic atresia and Hirschsprung's disease in the newborn: report of a new case and review of the literature.新生儿结肠闭锁与先天性巨结肠的关联:1例新病例报告及文献复习
Pediatr Surg Int. 2006 Mar;22(3):277-81. doi: 10.1007/s00383-005-1456-z. Epub 2005 Jul 14.
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Epidemiology. 2003 May;14(3):349-54.