Department of Respiratory Diseases, University Hospital Brno, Jihlavska 20, Brno, 62500, Czech Republic.
Faculty of Medicine, Masaryk University Brno, Kamenice 5, Brno, 62500, Czech Republic.
Orphanet J Rare Dis. 2023 Mar 20;18(1):62. doi: 10.1186/s13023-023-02671-z.
Cystic fibrosis (CF) is the most common genetic disease in the Caucasion population. Thanks to the CFTR modulators therapy, life expectancy will significantly improve. New therapeutic challenges can be expected, including diseases associated with ageing and higher incidence of cancer, as evidenced by recent epidemiological studies. The increasing incidence of tumors includes also breast cancer. The risk of breast cancer is higher in CF patients compared to the general population. Sex hormones, especially estrogens, also affect on the pathophysiology and immunology of the CF. Previous research, has demonstrated unequivocal survival rates for female CF patients compared to their male counterparts. Is demonstrated, that chemotherapy used for breast cancer affects the CFTR channel and CFTR modulator therapy has frequent side effects on breast tissue. In this review, we focus on the effects of female sex hormones on CF disease, pathophysiological relationships between CF and breast cancer, and the impact of antitumor treatment on both, malignant disease and CF. The potential for further investigation is also discussed.
囊性纤维化(CF)是白种人群体中最常见的遗传疾病。由于 CFTR 调节剂治疗,预期寿命将显著提高。新的治疗挑战可以预期,包括与衰老相关的疾病和更高的癌症发病率,最近的流行病学研究证明了这一点。肿瘤的发病率增加也包括乳腺癌。与普通人群相比,CF 患者的乳腺癌风险更高。性激素,尤其是雌激素,也会影响 CF 的病理生理学和免疫学。先前的研究表明,与男性 CF 患者相比,女性 CF 患者的生存率更高。研究表明,用于乳腺癌的化疗会影响 CFTR 通道,CFTR 调节剂治疗对乳腺组织常有副作用。在这篇综述中,我们重点关注女性性激素对 CF 疾病的影响、CF 和乳腺癌之间的病理生理关系,以及抗肿瘤治疗对恶性疾病和 CF 的影响。还讨论了进一步研究的潜力。