单侧肺动脉发育不全：咯血的一种罕见病因。
Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis.
作者信息
Wong Yen Shen, Abidin Zakhirati Zainol, Musa Aisya Natasya, Kadir Roqiah Fatmawati Abdul, Johari Bushra
机构信息
Faculty of Medicine, Universiti Teknologi MARA, Sungai Buloh, Malaysia.
Department of Radiology, Hospital Selayang, Batu Caves, Malaysia.
出版信息
Respir Med Case Rep. 2023 Mar 10;43:101834. doi: 10.1016/j.rmcr.2023.101834. eCollection 2023.
INTRODUCTION
Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations.
CASE
A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum.
CONCLUSION
Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings.
引言
单侧肺动脉缺如（UPAA）是一种罕见的先天性肺动脉畸形，由于胚胎发育过程中第六对主动脉弓缺如所致。由于临床表现多样，诊断可能具有挑战性。
病例
一名29岁双胎妊娠晚期女性出现大量咯血。计算机断层血管造影（CTA）显示右侧肺动脉单侧缺如，有多个扩张迂曲的支气管动脉为右肺供血。产后对支气管动脉进行了选择性栓塞。
结论
对于出现不明原因咯血且有典型UPAA影像学表现的患者，临床医生应高度怀疑侧支动脉出血。
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