Choi Yeonseok, Kang Noeul, Im Yunjoo, Choe Junsu, Kim Tae Jung, Kim Hojoong
Division of Pulmonary and Critical Care Medicine, Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, South Korea.
Department of Radiology and Center of Imaging Science, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, South Korea.
Respir Med Case Rep. 2018 Nov 1;26:14-16. doi: 10.1016/j.rmcr.2018.10.028. eCollection 2019.
Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly which can be symptomatic or even asymptomatic. Most of patients with isolated UPAA have mild symptoms and it is difficult to be diagnosed, especially when abnormal findings of chest radiograph are the first presentation. It is often misdiagnosed and is not considered during differential diagnosis. To make a diagnosis of UPAA, various imaging modalities including chest radiograph, computed tomography (CT), and angiography are used. We report a 33-year-old woman in pregnancy presented recurrent hemoptysis whose CT was postponed due to her pregnancy. Although CT is a useful diagnostic tool, chest radiograph could be used instead in pregnancy suggesting UPAA with a lot of information.
单侧肺动脉缺如（UPAA）是一种罕见的先天性异常，可表现为有症状或甚至无症状。大多数孤立性UPAA患者症状较轻，难以诊断，尤其是当胸部X线片的异常表现为首发症状时。它常被误诊，在鉴别诊断时也未被考虑。为了诊断UPAA，会使用包括胸部X线片、计算机断层扫描（CT）和血管造影在内的各种成像方式。我们报告一名33岁孕期女性反复咯血，因其怀孕CT检查被推迟。尽管CT是一种有用的诊断工具，但在孕期可使用胸部X线片替代，其能提供许多提示UPAA的信息。
