Reading David W, Oza Umesh
University of Texas Southwestern Medical School at Dallas (Reading) and the Department of Radiology, Baylor University Medical Center at Dallas (Oza).
Proc (Bayl Univ Med Cent). 2012 Apr;25(2):115-8. doi: 10.1080/08998280.2012.11928802.
Unilateral absence of a pulmonary artery (UAPA) is a rare condition with an estimated prevalence of 1 in 200,000 young adults. Most commonly, UAPA occurs in conjunction with cardiovascular abnormalities such as tetralogy of Fallot or cardiac septal defects, but it can also occur in an isolated manner. Patients with isolated UAPA can remain asymptomatic into late adulthood but usually report symptoms such as dyspnea or chest pain or suffer from hemoptysis or recurrent infections. Diagnosis can be difficult due to the rarity of the condition and its nonspecific presentation. We present a case of a 61-year-old man who presented for lung transplant evaluation and was found to have UAPA. Typical findings on chest radiograph, strategies for diagnosis, and available treatments are discussed.
单侧肺动脉缺如（UAPA）是一种罕见疾病，估计在每20万名年轻人中发生率为1例。最常见的情况是，UAPA与法洛四联症或心脏间隔缺损等心血管异常同时出现，但也可能单独发生。孤立性UAPA患者在成年后期可能仍无症状，但通常会报告呼吸困难、胸痛等症状，或出现咯血或反复感染。由于该疾病罕见且表现不具特异性，诊断可能会很困难。我们报告一例61岁男性患者，该患者因肺移植评估就诊，被发现患有UAPA。文中讨论了胸部X线片的典型表现、诊断策略和可用治疗方法。
