会阴部近端型上皮样肉瘤：一例报告及文献复习

Xia Shijun, Wu Wenjiang, Ma Lijuan

Shenzhen Hospital of Guangzhou University of Chinese Medicine, Shenzhen, China.

Shenzhen Traditional Chinese Medicine Anorectal Hospital, Shenzhen, China.

Front Oncol. 2023 Mar 6;13:1057466. doi: 10.3389/fonc.2023.1057466. eCollection 2023.

Proximal-type epithelioid sarcoma of the perineum is a rare soft-tissue malignancy, and only 55 cases have been reported in the English literature to date. This tumor has an indetectable early symptom and frequent recurrences. Here, we present the case of a 31-year-old man with proximal-type epithelioid sarcoma of the perineum who underwent wide excision. Further, we reviewed the current literature regarding differential diagnosis and management of this disease.

会阴部近端型上皮样肉瘤是一种罕见的软组织恶性肿瘤，迄今为止英文文献中仅报道了55例。该肿瘤早期症状不明显且复发频繁。在此，我们报告一例31岁患有会阴部近端型上皮样肉瘤的男性患者，其接受了广泛切除手术。此外，我们回顾了有关该疾病鉴别诊断和治疗的当前文献。