Yue Yuanyuan, Lu Ya, Ma Xiaojuan, Tang Zhongping, Cheng Yinrong
Department of Ultrasound, Chengdu First People's Hospital, Chengdu, Sichuan 610041, P.R. China.
Department of Pathology, West China Hospital, Sichuan University, Chengdu, Sichuan 610065, P.R. China.
Mol Clin Oncol. 2018 Nov;9(5):507-510. doi: 10.3892/mco.2018.1708. Epub 2018 Sep 3.
Proximal-type epithelioid sarcoma (PES) of the vulva is an exceedingly rare malignant soft tissue tumor. We herein present the case of a 41-year-old female patient who presented to our hospital with complaints of a painless mass in the right mons pubis that she had first noticed 3 years prior. Ultrasonographic (US) and color Doppler ultrasonographic (CDUS) examination revealed a solid mass with well-defined, homogeneous hypoechoic structure and quite hypervascular on CDUS. The results of the immunohistochemical examination confirmed the diagnosis of vulvar PES (myxoid variant). The patient was treated with wide local excision and remained recurrence- and metastasis-free at 9 months postoperatively. Although cases of PES in the pelvic region had been previously reported, to the best of our knowledge, the US or CDUS findings of PES of the vulva have not been described to date.
外阴近端型上皮样肉瘤（PES）是一种极其罕见的恶性软组织肿瘤。我们在此报告一例41岁女性患者，她因右侧耻骨前无痛性肿块前来我院就诊，该肿块她3年前首次发现。超声（US）和彩色多普勒超声（CDUS）检查显示为实性肿块，边界清晰，结构均匀呈低回声，CDUS显示血管丰富。免疫组化检查结果确诊为外阴PES（黏液样变型）。患者接受了广泛局部切除，术后9个月无复发和转移。尽管此前已有盆腔区域PES病例的报道，但据我们所知，迄今为止尚未对外阴PES的US或CDUS表现进行过描述。
