[Late onset cystinosis. Apropos of a case].
作者信息
Hamdoun S, Lebon P, Nivet H, Beaufils H, Babinet F, Kernaonet E
机构信息
Service de Néphrologie-Dialyse, Centre Hospitalier Général, Le Mans.
出版信息
Nephrologie. 1987;8(4):193-5.
PMID:3696368
Abstract
This report concerns a new case of late onset cystinosis with heavy proteinuria. Renal biopsy showed focal segmental glomerular hyalinosis and the usual tubular and glomerular lesions of cystinosis. The pathogenesis of glomerular hyalinosis remains unclear.
摘要
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