Couillandre Pauline, Lewalle Philippe, Benghiat Samantha Fleur, Salaroli Adriano
Unité de Néonatologie-Réanimation Néonatale, Hôpital Yves Le Foll, St Brieuc, France.
Hematology Department, Jules Bordet Institute, Université Libre de Bruxelles, 1070 Brussels, Belgium.
Eur J Case Rep Intern Med. 2023 Mar 9;10(3):003722. doi: 10.12890/2023_003722. eCollection 2023.
Myomatous erythrocytosis syndrome (MES) is a rare gynaecological condition associated with the presence of a uterine fibroid and isolated polycythaemia. The main characteristic of MES is that haemoglobin returns to a normal level after removal of the myoma. MES is poorly known and still not fully understood. This case report describes the history of a patient with MES with surprising erythrocytosis resolution after myomectomy.
A case of myomatous erythrocytosis syndrome with a normal erythropoietin level is described, adding to the scarce literature; the mediator responsible for the erythrocytosis is not yet known.This is a rare presentation of a common condition: erythrocytosis and uterine fibroids are frequent in the general population but are only anecdotally correlated.Delayed diagnosis led to unnecessary aggressive treatment with the aim of reducing the haematocrit level to below 45%.
子宫肌瘤性红细胞增多症综合征(MES)是一种罕见的妇科疾病,与子宫肌瘤和单纯性红细胞增多症有关。MES的主要特征是切除肌瘤后血红蛋白恢复到正常水平。MES鲜为人知,仍未被完全理解。本病例报告描述了一名MES患者的病史,该患者在肌瘤切除术后红细胞增多症得到了惊人的缓解。
描述了一例促红细胞生成素水平正常的子宫肌瘤性红细胞增多症综合征病例,补充了稀少的文献资料;导致红细胞增多症的介质尚不清楚。这是一种常见疾病的罕见表现:红细胞增多症和子宫肌瘤在普通人群中很常见,但只是偶尔相关。延迟诊断导致了旨在将血细胞比容水平降至45%以下的不必要的积极治疗。