da Silveira Caroline Ferreira da Silva Mazeto Pupo, Mauricio Alejandra Villanueva, da Silva Mazeto Gláucia Maria Ferreira, Okoshi Katashi, Borges Vera Therezinha Medeiros, Bazan Silmeia Garcia Zanati
Internal Medicine Department, Botucatu Medical School, UNESP, Rua Dr Joao Queiroz Reis, 700, Vila Sonia, Botucatu, Sao Paulo, CEP 18607-010, Brazil.
Gynecology and Obstetrics Department, Botucatu Medical School, UNESP, Botucatu, Sao Paulo, Brazil.
Radiol Case Rep. 2023 Mar 16;18(5):1945-1948. doi: 10.1016/j.radcr.2023.02.017. eCollection 2023 May.
Pentalogy of Fallot (PoF) is a congenital heart disease comprising tetralogy of Fallot plus an atrial septal defect (ASD). Patients are diagnosed early in life and submitted to reparative surgery. Without it, the prognosis is poor. This female patient, initially diagnosed with transposition of great arteries (TGA), ASD and a ventricular septal defect, got pregnant at 26 years old and had an early delivery due to fetal distress. She resumed follow-up, and her last echocardiogram put in doubt the diagnosis of TGA. Cardiac CT then revealed a PoF as well as pulmonary arteriovenous fistulas and a persistent left superior vena cava.
法洛五联症（PoF）是一种先天性心脏病，由法洛四联症加上房间隔缺损（ASD）组成。患者在幼年时被诊断出来并接受修复手术。如果不进行手术，预后很差。这位女性患者最初被诊断为大动脉转位（TGA）、房间隔缺损和室间隔缺损，26岁时怀孕，因胎儿窘迫早产。她恢复了随访，她最后一次超声心动图检查使大动脉转位的诊断受到质疑。心脏CT随后显示为法洛五联症以及肺动静脉瘘和持续左上腔静脉。
