继发于家族性渗出性玻璃体视网膜病变伴慢性渗出性视网膜脱离的闪辉性玻璃体液化的病理结果
Pathological Findings of Synchysis Scintillans Secondary to Familial Exudative Vitreoretinopathy With Chronic Exudative Retinal Detachment.
作者信息
Lin James, Garcia Armando, Chen Ying, Dubovy Sander, Lee Wendy, Kopplin Laura J, Berrocal Audina
机构信息
Department of Ophthalmology, Bascom Palmer Eye Institute, Miller School of Medicine, University of Miami, Miami, FL, USA.
Department of Ophthalmology, Medical College of Wisconsin, Milwaukee, WI, USA.
出版信息
J Vitreoretin Dis. 2019 Oct 16;4(2):163-166. doi: 10.1177/2474126419880385. eCollection 2020 Mar-Apr.
PURPOSE
We describe a unique case of synchysis scintillans in a 23-year-old woman with a history of chronic exudative retinal detachment in the setting of familial exudative vitreoretinopathy.
METHODS
Fundus and slit-lamp photographs were obtained at presentation, and pathological studies were performed on the enucleated specimen to confirm the diagnosis.
RESULTS
Synchysis scintillans is a degenerative condition of cholesterol deposition that affects severely damaged eyes, often as a result of chronic vitreous hemorrhage or retinal detachment. In this case, synchysis scintillans presented as crystals in the anterior chamber in the setting of a chronic retinal detachment. After enucleation, there were noted to be cholesterol slits on pathological correlation, confirming the diagnosis.
CONCLUSIONS
This case demonstrates the importance of clinical pathological correlation in the diagnosis of synchysis scintillans migrating into the anterior chamber.
目的
我们描述了一名23岁女性的闪辉性玻璃体液化的独特病例，该女性有家族性渗出性玻璃体视网膜病变背景下的慢性渗出性视网膜脱离病史。
方法
就诊时拍摄了眼底和裂隙灯照片，并对摘除的标本进行了病理研究以确诊。
结果
闪辉性玻璃体液化是一种胆固醇沉积的退行性疾病，常因慢性玻璃体出血或视网膜脱离而影响严重受损的眼睛。在本病例中，闪辉性玻璃体液化表现为慢性视网膜脱离情况下前房内的晶体。摘除眼球后，经病理检查发现有胆固醇裂隙，从而确诊。
结论
该病例证明了临床病理相关性在诊断迁移至前房的闪辉性玻璃体液化中的重要性。
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