Department of Urology, Sri Sathya Sai Institute of Higher Medical Sciences, Puttaparthi, Andhra Pradesh, India.
Department of Urology, Sri Sathya Sai Institute of Higher Medical Sciences, Puttaparthi, Andhra Pradesh, India.
Urology. 2023 Aug;178:138-142. doi: 10.1016/j.urology.2023.03.036. Epub 2023 Apr 5.
Exstrophy variants are uncommon developmental anomalies of the bladder; the variants involving only the bladder neck are extremely rare. There are only three case reports of inferior vesical fissure (IVF) to date, and usually it's uncommonly associated with other malformations. A combination of inferior vesical fistula (IVF) as an exstrophy variant with urethral atresia and anorectal malformation has not been described previously. We report a case of IVF in a 4-year-old male previously operated for anorectal malformation who was managed with fistula closure with bladder neck reconstruction of lay open of stenosed urethra. Recognition of the exstrophy variant is important because the treatment and prognosis are very different.
膀胱外翻变体是一种罕见的膀胱发育异常;仅涉及膀胱颈部的变体极其罕见。迄今为止,只有三个下膀胱裂隙 (IVF) 的病例报告,并且通常很少与其他畸形相关。下膀胱瘘 (IVF) 作为膀胱外翻变体与尿道闭锁和肛门直肠畸形的组合以前没有描述过。我们报告了一例 4 岁男性 IVF 的病例,该患者曾因肛门直肠畸形接受过手术治疗,采用膀胱颈部重建的方法对狭窄的尿道进行了开放性手术,同时闭合了瘘管。认识到外翻变体很重要,因为治疗和预后有很大的不同。