Department of Radiology, Huizhou Central People's Hospital, Huizhou, Guangdong, China.
Department of Ultrasound, Huizhou Central People's Hospital, Huizhou, Guangdong, China.
Technol Health Care. 2023;31(S1):45-54. doi: 10.3233/THC-236005.
Abdominal wall desmoid-type fibromatoses (AWDF) are occasionally encountered in clinical work, but related CT reports are rare, and most cases were misdiagnosed as malignant tumors.
We aimed to determine the diagnostic value of multislice computed tomography (MSCT) in relation to the clinical diagnosis of AWDF.
The medical records of 14 patients whose pathology results provided initial confirmation of AWDF were reviewed, and data describing their clinical characteristics, tumors' MSCT characteristics, and the condition of the surrounding tissues were analyzed and summarized retrospectively. Intraobserver and interobserver reproducibilities were evaluated.
AWDF tended to occur in women of childbearing age (24-32 years). They occurred more frequently during the first year following pregnancy. The mean disease duration was 5.64 ± 3.78 months. All isolated tumors were growing along the musculoaponeurotic layer, and their maximum diameters were between 32 and 76 mm. Tumors' capsules were incomplete, and although the tumors infiltrated the surrounding muscles, the surrounding fat tissue and vessels were not infiltrated. None of the patients' tumors showed cystic degeneration, calcification, necrosis, or peritumoral edema. The tumors had slightly lower densities on the pre-contrast enhancement scans and mild-to-moderate enhancement after contrast enhancement. All tumors contained ribbon-like structures, and approximately 65% of the tumors encircled vascular structures.
Dual-phase contrast-enhanced MSCT scans were associated with a high level of diagnostic efficacy for AWDF. The abdominal wall masses grew along the musculoaponeurotic layer, which, together with the ribbon-like structures within the tumors, should prompt clinicians to consider the presence of AWDF.
腹壁韧带样纤维瘤病（AWDF）在临床工作中偶尔会遇到，但相关 CT 报道很少，大多数病例被误诊为恶性肿瘤。
旨在确定多层螺旋 CT（MSCT）在 AWDF 临床诊断中的诊断价值。
回顾性分析了 14 例经病理证实为 AWDF 的患者的病历资料，分析并总结了其临床特征、肿瘤 MSCT 特征及周围组织情况等资料，并评估了观察者内和观察者间的可重复性。
AWDF 多发生于育龄期女性（24-32 岁），产后 1 年内多见，平均病程为 5.64±3.78 个月。所有孤立性肿瘤均沿肌筋膜层生长，最大径为 32-76mm，肿瘤包膜不完整，肿瘤虽浸润周围肌肉，但周围脂肪组织及血管未受累。无一例患者肿瘤出现囊变、钙化、坏死及瘤周水肿。平扫时肿瘤密度稍低于周围肌肉，增强扫描呈轻-中度强化。所有肿瘤内均见条索状结构，约 65%的肿瘤环绕血管结构。
AWDF 的双期增强 MSCT 扫描具有较高的诊断效能。腹壁肿块沿肌筋膜层生长，肿瘤内的条索状结构，均应提示临床医生考虑 AWDF 的存在。
