Department of Radiology, Armed Forces Institute of Radiological Imaging, Rawalpindi, Pakistan.
Department of Thoracic Surgery, Kalsoom International Hospital, Islamabad, Pakistan.
J Pak Med Assoc. 2023 Apr;73(4):922-924. doi: 10.47391/JPMA.6669.
Lymphangiomas, also known as lymphatic malformations, are rare non-neoplastic lesions of vascular origin showing lymphatic differentiation. These are most commonly reported in children within the neck and axillary region; however, mediastinum remains the commonest site in adults whereby diagnosis is usually incidental on imaging done for non-specific symptoms. Radiologically, these lesions are well-defined multicystic non-enhancing masses, with CT attenuation values ranging from simple to complex fluid and fat. Being benign, these mostly present clinically either due to mass effect exerted on structures, secondarily infected or developing intra lesion haemorrhage. We present a rare case of mediastinal lymphangioma with secondary hilar and intrapulmonary extension in a middle-aged female presenting with occasional haemoptysis and shortness of breath. The patient underwent thoracotomy with complete dissection of the mediastinal tumour, per operative Bleomycin administration in pulmonary component, and made subsequent uneventful post-operative recovery.
淋巴管瘤,又称淋巴管畸形,是一种罕见的非肿瘤性血管来源病变,表现为淋巴管分化。这些病变最常见于儿童的颈部和腋窝区域;然而,在成年人中,纵隔仍然是最常见的部位,诊断通常是在因非特异性症状进行影像学检查时偶然发现的。放射学上,这些病变为界限清楚的多房性非增强性肿块,CT 衰减值从单纯性到复杂性液体和脂肪不等。由于这些病变是良性的,因此大多数情况下是由于对结构的压迫、继发感染或内部出血导致的临床症状。我们报告了一例罕见的中年女性纵隔淋巴管瘤病例,伴有继发性肺门和肺内延伸,表现为偶尔咯血和呼吸急促。患者接受了开胸手术,完全切除纵隔肿瘤,术中在肺部分布博来霉素,并随后顺利恢复。