[Vegetative and trophic disorders and functional status of the sympatho-adrenal system in Rossolimo-Curschmann-Batten-Steinert myotonic dystrophy].

In a comprehensive examination of 16 patients with the Rossolimo-Curschmann-Steinert-Batten myotonic dystrophy the authors determined catecholamine levels in the adrenergic structures of skeletal muscles, levels of adrenaline and noradrenaline in the blood and their daily excretion with the urine. The findings showed elevated concentrations of catecholamines in the adrenergic structures of skeletal muscles which suggests an intensified diffusion of catecholamines from adrenergic structures into the adjacent muscular tissue. The sympathoadrenal system functioned under stress. Myotonic dystrophy was associated with disturbances of both central and peripheral mechanisms of vegetative regulation of muscular activity.