1例罕见的巨大肠系膜脂肪母细胞瘤导致1名8个月大儿童出现腹部肿块。
A rare case of giant mesenteric lipoblastoma causing an abdominal mass in an 8-month-old child.
作者信息
Laarif Souha, Trabelsi Fatma, Saadi Cyrine, Abdallah Rabiaa Ben, Hellal Youssef, Kaabar Nejib
机构信息
Pediatric Surgery Department, Habib Thameur Hospital, Tunis, Tunisia.
Pediatric Surgery Department, Habib Thameur Hospital, Tunis, Tunisia.
出版信息
Int J Surg Case Rep. 2023 May;106:108072. doi: 10.1016/j.ijscr.2023.108072. Epub 2023 Mar 25.
INTRODUCTION AND IMPORTANCE
Giant mesenteric lipoblastoma (LB) is a rare and benign tumor derived from adipocytes. It may imitate malignant tumors, and its diagnosis is challenging before surgery. The diagnosis can be guided by imaging studies but cannot be confirmed. Just a few cases of lipoblastoma originating from the mesentery are reported in the literature.
CASE PRESENTATION
We present a case of a rare giant lipoblastoma arising from the mesentery of an 8-month-old boy who consulted our emergency department for an incidentally discovered abdominal mass.
CLINICAL DISCUSSION
LB is most common in the first decade of life, with a high incidence in boys. LBs are generally found in the trunk and extremities. Intra-abdominal locations are rare; however, intraperitoneal tumors generally reach larger dimensions.
CONCLUSIONS
Tumors that arise in the abdomen are usually larger and may be discovered by physical exam as an abdominal mass and may cause compression symptoms.
引言与重要性
巨大肠系膜脂肪母细胞瘤（LB）是一种源自脂肪细胞的罕见良性肿瘤。它可能类似恶性肿瘤，术前诊断具有挑战性。影像学检查可用于指导诊断，但无法确诊。文献中仅报道了少数起源于肠系膜的脂肪母细胞瘤病例。
病例介绍
我们报告一例罕见的巨大脂肪母细胞瘤，起源于一名8个月大男童的肠系膜，该患儿因偶然发现腹部肿块前来我院急诊科就诊。
临床讨论
脂肪母细胞瘤在生命的第一个十年最为常见，男性发病率较高。脂肪母细胞瘤通常位于躯干和四肢。腹腔内位置罕见；然而，腹腔内肿瘤通常体积更大。
结论
发生在腹部的肿瘤通常更大，可能通过体格检查发现腹部肿块，并可能引起压迫症状。
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