一例室间隔完整且肺动脉分支交叉的共同动脉干病例报告。
A case report of truncus arteriosus with intact ventricular septum and crossed branch pulmonary arteries.
作者信息
Davidson Hannah, Seco Michael, Asakai Hiroko, Liava'a Matthew
机构信息
Heart Centre for Children, The Children's Hospital at Westmead, Cnr Hawkesbury Rd & Hainsworth St, Westmead NSW 2145, Australia.
Discipline of Child and Adolescent Health, The Children's Hospital at Westmead Clinical School, Sydney Medical School, Haweksbury Road, Sydney, Westmead NSW 2145, Australia.
出版信息
Eur Heart J Case Rep. 2023 Mar 29;7(4):ytad134. doi: 10.1093/ehjcr/ytad134. eCollection 2023 Apr.
BACKGROUND
Truncus arteriosus (TA) or persistent arterial trunk describes the presence of a solitary arterial trunk arising from the base of the heart, supported by a common ventriculoarterial junction. The trunk gives rise to the coronary arteries, systemic arteries, and at least one pulmonary artery. Truncus arteriosus is a rare congenital cardiac disease, and even rarer is the absence of ventricular septal defect.
CASE SUMMARY
We report a case of a 2-day-old infant who presented with cyanosis and a cardiac murmur. He was diagnosed with TA with intact ventricular septum (IVS), as well as crossed pulmonary arteries which was identified on pre-operative imaging. We describe the surgical management and short-term follow-up.
DISCUSSION
Our clinical case demonstrates a unique diagnosis and management of TA with IVS identified by pre-operative imaging with good surgical outcome.
背景
动脉干（TA）或永存动脉干是指由心脏基部发出的单一动脉干，由共同的心室动脉连接支持。该动脉干发出冠状动脉、体循环动脉和至少一条肺动脉。动脉干是一种罕见的先天性心脏病，而没有室间隔缺损的情况更为罕见。
病例摘要
我们报告一例2日龄婴儿，表现为青紫和心脏杂音。他被诊断为室间隔完整（IVS）的动脉干，术前影像学检查发现肺动脉交叉。我们描述了手术治疗及短期随访情况。
讨论
我们的临床病例展示了通过术前影像学检查确诊的室间隔完整动脉干的独特诊断和治疗方法，手术效果良好。
Zotero 插件