Department of Neurology, Mid-Atlantic Permanente Medical Group, Rockville, MD, USA.
Department of Research, Mid-Atlantic Permanente Research Institute, Rockville, MD, USA.
Am J Case Rep. 2023 May 8;24:e939035. doi: 10.12659/AJCR.939035.
BACKGROUND Anti-PL-12 syndrome is a rare form of myositis. Amyotrophic lateral sclerosis (ALS) is the commonest of the motor neuron disorders. However, the 2 conditions have not been reported to occur together in a single individual. This case report describes a patient who was diagnosed with anti-PL-12 anti-synthetase syndrome and then subsequently was diagnosed with ALS. CASE REPORT A 55-year-old male patient had anti-PL-12 syndrome and ALS occurring together. The patient initially presented with musculoskeletal complaints and was diagnosed with anti-PL-12 syndrome. He later went on to develop shortness of breath. Neurophysiological testing subsequently confirmed ALS as the patient experienced worsening muscle weakness over a 2-year period. A muscle biopsy performed showed neurogenic and myopathic process. The patient eventually lost the ability to ambulate without mobility assistance and suffered cardiac arrest due to complications from ALS, specifically diaphragmatic dysfunction. CONCLUSIONS This case report represents the first documented case of a patient having both anit-PL-12 syndrome and ALS together. It has been suggested that having an autoimmune disease (AID) may increase the subsequent risk of developing ALS. Previous studies did not conduct evaluation to ascertain serological markers for AS antibodies. Lab tests were rechecked and revalidated multiple times in separate facilities for confirmation of results in case of initial lab error. This may suggest a common etiology for both anti-PL-12 syndrome and ALS.
抗-PL-12 综合征是一种罕见的肌炎形式。肌萎缩侧索硬化症(ALS)是最常见的运动神经元疾病。然而,这两种情况尚未在单个个体中同时报告。本病例报告描述了一名被诊断患有抗-PL-12 抗合成酶综合征的患者,随后又被诊断患有 ALS。
一名 55 岁男性患者同时患有抗-PL-12 综合征和 ALS。患者最初出现肌肉骨骼投诉,并被诊断为抗-PL-12 综合征。后来,他开始出现呼吸急促。神经生理学测试随后证实 ALS 是患者在 2 年内肌肉无力恶化。进行的肌肉活检显示出神经源性和肌病过程。患者最终失去了在没有移动辅助的情况下行走的能力,并因 ALS 的并发症(特别是膈肌功能障碍)而发生心脏骤停。
本病例报告代表了首例同时患有抗-PL-12 综合征和 ALS 的患者。有研究表明,患有自身免疫性疾病(AID)可能会增加随后发展为 ALS 的风险。以前的研究没有进行评估以确定抗 AS 抗体的血清学标志物。为了确认初始实验室错误,在不同的设施中多次重新检查和重新验证实验室测试以确认结果。这可能表明抗-PL-12 综合征和 ALS 具有共同的病因。