Beijing Institute of Otolaryngology, Beijing Tongren Hospital, Capital Medical University.
Department of Radiology, Beijing Tongren Hospital, Capital Medical University, Beijing, PR China.
Otol Neurotol. 2023 Jun 1;44(5):e295-e299. doi: 10.1097/MAO.0000000000003875.
Rudimentary otocyst (RO) is characterized by an otic capsule without an internal auditory canal, which is considered a contraindication to cochlear implantation (CI). In this study, we were the first to report two patients with ROs who underwent CI.
Two patients (18 months old and 2 years old) presenting with bilateral congenital hearing loss were diagnosed with ROs.
CI was performed. The transmastoid slotted labyrinthotomy approach was used with customized MED-EL electrode arrays.
Categorical auditory performance, infant-toddler meaningful auditory integration of sound, the speech intelligibility rating, and meaningful use of speech scale.
Both children could understand common phrases and had intelligible, connected speech 2 years after CI.
With proper indication, surgical approach and postoperative training, a child with an RO may benefit from CI.
初级耳囊（RO）的特征为无内耳迷路的耳囊，这被认为是人工耳蜗植入（CI）的禁忌。本研究中，我们首次报道了 2 例 RO 患者接受 CI。
2 例（18 个月和 2 岁）双侧先天性听力损失患儿诊断为 RO。
进行 CI。采用经乳突开槽迷路切开术，使用定制的 MED-EL 电极阵列。
分类听觉表现、婴幼儿有意义的声音综合听觉、言语可懂度分级和言语的有效使用量表。
2 例患儿 CI 后 2 年均可理解常用短语，言语可懂度高、连贯。
在适当的适应证、手术方法和术后训练下，RO 患儿可能受益于 CI。
