Radeloff Katrin, Sandmann Pascale, Klüner Claudia, Radeloff Andreas
Universitätsklinik für Hals-Nasen-Ohren-Heilkunde, Evangelisches Krankenhaus Oldenburg, Steinweg 13-17, 26122, Oldenburg, Deutschland.
Klinische Audiologie, Universitätsklinik für Hals-Nasen-Ohren-Heilkunde, Evangelisches Krankenhaus Oldenburg, Oldenburg, Deutschland.
HNO. 2024 Nov;72(11):800-808. doi: 10.1007/s00106-024-01507-x. Epub 2024 Aug 28.
Cochlear implants (CIs) are the treatment of choice for hearing rehabilitation in children with congenital or acquired profound hearing loss or deafness in order to ensure appropriate speech development and avoid social deprivation. However, in the case of a radiologically detectable malformation of the inner ear structures and potentially associated hypo- or aplasia of the vestibulocochlear nerve, application of a CI is either not possible, or the functional outcome may be of limited predictability. In addition, the risk of surgical complications is also increased in these patients. Counseling parents and developing an appropriate individual therapeutic decision can therefore be a major challenge for the medical team. The current paper is intended to provide support in this regard. It presents criteria for various inner ear malformations and discusses possible treatment options.
人工耳蜗（CI）是先天性或后天性重度听力损失或耳聋儿童听力康复的首选治疗方法，以确保适当的言语发育并避免社交剥夺。然而，如果内耳结构在放射学上可检测到畸形，以及潜在相关的前庭蜗神经发育不全或发育不全，那么要么无法应用CI，要么功能结果的可预测性可能有限。此外，这些患者手术并发症的风险也会增加。因此，为家长提供咨询并做出适当的个体化治疗决策可能是医疗团队面临的一项重大挑战。本文旨在在这方面提供支持。它提出了各种内耳畸形的标准，并讨论了可能的治疗选择。
