Thanopoulos B D, Fisher E A, Hastreiter A R
Br Heart J. 1986 Jun;55(6):602-4. doi: 10.1136/hrt.55.6.602.
Clinical, haemodynamic, angiocardiographic, and necropsy findings are reported in a newborn infant who presented with typical findings of the severe form of the syndrome of absent pulmonary valve. In addition to the usual findings of aneurysmal dilatation of the pulmonary arteries, pulmonary insufficiency, and stenosis, this patient had an intact ventricular septum and large ductus arteriosus. The former is a rare finding and the latter is not known to have been reported in a patient with the severe form of this syndrome.
本文报告了一名患有严重型肺动脉瓣缺如综合征典型表现的新生儿的临床、血流动力学、心血管造影及尸检结果。除了肺动脉瘤样扩张、肺动脉瓣关闭不全和狭窄等常见表现外，该患者室间隔完整且动脉导管粗大。前者是一种罕见发现，而后者在患有该综合征严重型的患者中尚无报道。
