Antonelli D, Mazor G, Avni G
Cardiology. 1986;73(3):160-3. doi: 10.1159/000174001.
A case of a month-old baby admitted for dyspnea and cyanosis, is described. His past history consisted of only mild cyanosis during crying. On physical examination nail beds and lips were cyanotic; on heart auscultation the pulmonary second sound was single. The chest X-ray showed a decreased pulmonary vascularity; the ECG demonstrated extreme right axis deviation (-170 degrees). Capillary gas analysis revealed hypoxic metabolic acidosis. Ten hours after his admission the child suddenly died. The anatomicopathological examination stated the diagnosis of double outlet right ventricle (DORV), infundibular pulmonary stenosis and common atrioventricular canal (transitional type). When clinical findings are compatible with DORV the ECG could be of value in establishing the presence of common atrioventricular canal when extreme right axis deviation is found.
本文描述了一例因呼吸困难和发绀入院的1月龄婴儿。其既往史仅为哭闹时轻度发绀。体格检查发现甲床和嘴唇发绀；心脏听诊显示肺动脉第二心音单一。胸部X线显示肺血管纹理减少；心电图显示极度右轴偏移（-170度）。毛细血管血气分析显示低氧代谢性酸中毒。入院10小时后，患儿突然死亡。解剖病理学检查确诊为右心室双出口（DORV）、漏斗部肺动脉狭窄和共同房室通道（过渡型）。当临床发现与DORV相符时，若发现极度右轴偏移，心电图对确定是否存在共同房室通道可能有价值。
