并存变异与右冠状动脉异常起源伴复发性室性心动过速
Coexisting Variant and the Anomalous Origin of the Right Coronary Artery Presenting with Recurrent Ventricular Tachycardia.
作者信息
Hernandez Ilsen E, Prakash Atul
机构信息
Medicine/Cardiology Department, St. Mary's General Hospital, Passaic, NJ, USA.
出版信息
J Innov Card Rhythm Manag. 2023 May 15;14(5):5431-5434. doi: 10.19102/icrm.2023.14051. eCollection 2023 May.
Abstract
A 49-year-old woman presented with recurrent palpitations and presyncope. Monitoring revealed recurrent non-sustained ventricular tachycardia (VT) episodes. Cardiac catheterization showed the right coronary artery originating from the left coronary cusp. Cardiac computerized tomography revealed the course between the aorta and the pulmonary artery. Despite surgical correction, VT persisted. Genetic testing revealed a rare BCL2-associated athanogene 3 () variant associated with dilated cardiomyopathy.
摘要
一名49岁女性出现反复心悸和接近晕厥的症状。监测发现有反复的非持续性室性心动过速（VT）发作。心脏导管检查显示右冠状动脉起源于左冠状动脉瓣叶。心脏计算机断层扫描显示了主动脉和肺动脉之间的走行。尽管进行了手术矫正，室性心动过速仍持续存在。基因检测发现一种罕见的与扩张型心肌病相关的BCL2相关热稳定蛋白3（）变异体。
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