Silva R, Cogbill T H, Hansbrough J F, Zapata-Sirvent R L, Harrington D S
Int Surg. 1986 Jan-Mar;71(1):48-50.
Ehlers-Danlos syndrome is a rare genetically determined disorder of connective tissue. Such patients often present challenges in clinical diagnosis and management. Dramatic life-threatening presentations include gastrointestinal perforation and vascular rupture, both occurring in the patient described. This case illustrates diagnostic features and therapeutic maneuvers important in the management of such complications of this disorder.
埃勒斯-当洛综合征是一种罕见的由遗传决定的结缔组织疾病。这类患者在临床诊断和管理方面常常面临挑战。严重的危及生命的表现包括胃肠道穿孔和血管破裂，在所描述的患者中这两种情况都出现了。该病例说明了在这种疾病并发症管理中重要的诊断特征和治疗手段。
