[一例成人肝脏未分化胚胎性肉瘤]

[A Case of Hepatic Undifferentiated Embryonal Sarcoma in an Adult].

作者信息

Miura Tomoya, Ottomo Shigeru, Sato Ataru, Fujita Shouta, Sato Mamoru, Ajiki Takashi, Akahira Junichi, Yamauchi Junichirou

机构信息

Dept. of Gastrointestinal Surgery, Digestive Disease Center, Sendai Kousei Hospital.

出版信息

Gan To Kagaku Ryoho. 2023 May;50(5):639-641.

PMID:37218329

Abstract

A 20-year-old woman was admitted with abdominal pain and a cystic liver tumor. A hemorrhagic cyst was suspected. Contrast-enhanced computed tomography(CT)and magnetic resonance imaging(MRI)revealed a space-occupying solid mass in the right lobule. Positron emission tomography(PET)-CT revealed 18F-fluorodeoxyglucose uptake in the tumor. We performed a right hepatic lobectomy. Histopathological evaluation of the resected tumor revealed an undifferentiated embryonal sarcoma of the liver(UESL). The patient refused adjuvant chemotherapy but showed no recurrence 30 months postoperatively. UESL is a rare malignant mesenchymal tumor that occurs in infants and children. It is extremely rare and is associated with poor prognosis in adults. In this report, we described a case of adult UESL.

摘要

一名20岁女性因腹痛和肝脏囊性肿瘤入院。怀疑为出血性囊肿。增强计算机断层扫描（CT）和磁共振成像（MRI）显示右叶有一个占位性实性肿块。正电子发射断层扫描（PET）-CT显示肿瘤中有18F-氟脱氧葡萄糖摄取。我们进行了右肝叶切除术。对切除肿瘤的组织病理学评估显示为肝脏未分化胚胎性肉瘤（UESL）。患者拒绝辅助化疗，但术后30个月未出现复发。UESL是一种罕见的恶性间充质肿瘤，发生于婴幼儿和儿童。在成人中极为罕见且预后不良。在本报告中，我们描述了一例成人UESL病例。