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免疫球蛋白缺乏症患者的 COVID-19 肺炎伴游走性表现:两例病例报告及文献复习。

COVID-19 Pneumonia with Migratory Pattern in Agammaglobulinemic Patients: A Report of Two Cases and Review of Literature.

机构信息

Unit of Infectious and Tropical Diseases, Department of Clinical and Experimental Sciences, University of Brescia and ASST Spedali Civili di Brescia, 25123 Brescia, Italy.

Department of Medical and Surgical Specialties, Radiological Sciences and Public Health, University of Brescia and ASST Spedali Civili of Brescia, 25123 Brescia, Italy.

出版信息

Tomography. 2023 Apr 23;9(3):894-900. doi: 10.3390/tomography9030073.

DOI:10.3390/tomography9030073
PMID:37218933
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10204514/
Abstract

X-linked agammaglobulinemia (XLA) is a primary immunodeficiency characterized by marked reduction in serum immunoglobulins and early-onset infections. Coronavirus Disease-2019 (COVID-19) pneumonia in immunocompromised patients presents clinical and radiological peculiarities which have not yet been completely understood. Very few cases of agammaglobulinemic patients with COVID-19 have been reported since the beginning of the pandemic in February 2020. We report two cases of migrant COVID-19 pneumonia in XLA patients.

摘要

X 连锁无丙种球蛋白血症(XLA)是一种以血清免疫球蛋白显著减少和早期感染为特征的原发性免疫缺陷病。免疫功能低下患者的 2019 冠状病毒病(COVID-19)肺炎具有尚未完全了解的临床和影像学特征。自 2020 年 2 月大流行开始以来,报告的 COVID-19 伴无丙种球蛋白血症患者的病例非常少。我们报告了 2 例 XLA 患者的移民 COVID-19 肺炎病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/53ce/10204514/5e76fd4af049/tomography-09-00073-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/53ce/10204514/b9b2ff59992d/tomography-09-00073-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/53ce/10204514/5e76fd4af049/tomography-09-00073-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/53ce/10204514/b9b2ff59992d/tomography-09-00073-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/53ce/10204514/5e76fd4af049/tomography-09-00073-g002.jpg

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Front Immunol. 2022 Nov 24;13:1057065. doi: 10.3389/fimmu.2022.1057065. eCollection 2022.
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COVID-19-related health outcomes in people with primary immunodeficiency: A systematic review.原发性免疫缺陷患者的 COVID-19 相关健康结局:系统评价。
Clin Immunol. 2022 Oct;243:109097. doi: 10.1016/j.clim.2022.109097. Epub 2022 Aug 13.
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Specific T-cell responses for guiding treatment with convalescent plasma in severe COVID-19 and humoral immunodeficiency: a case report.
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