Ballanger P, Petit J, Thomas G, Tauzin-Fin P
Ann Urol (Paris). 1986;20(3):195-200.
Based on four new cases of emphysematous pyelonephritis, the authors review a total or 59 interpretable cases of this rare disease reported in the literature. The general features of this condition are as follows: diabetic women are most frequently affected, the clinical context is generally very serious, the diagnosis is based on X-ray findings, radiating or crescent-shaped radiolucent gas images are observed with a non-functioning kidney on intravenous pyelography. CT scan was performed in two cases and confirmed the presence of air in the renal parenchyma and provided a better evaluation of the extension into the perirenal space. The only effective treatment is nephrectomy which has been able to improve the prognosis of this very serious disease, especially as the characteristic necrosis observed on histology leaves no hope of functional recovery.
基于4例气肿性肾盂肾炎新病例，作者回顾了文献中报道的总共59例可解读的该罕见疾病病例。这种病症的一般特征如下：糖尿病女性最常受累，临床情况通常非常严重，诊断基于X线检查结果，静脉肾盂造影显示无功能的肾脏出现放射状或新月形透光气体影像。对2例患者进行了CT扫描，证实肾实质内存在气体，并能更好地评估其向肾周间隙的蔓延情况。唯一有效的治疗方法是肾切除术，这能够改善这种非常严重疾病的预后，特别是因为组织学上观察到的特征性坏死使得功能恢复无望。
