Abide Zakaria, Sif Nasr Karima, Kaddouri Soufiane, Edderai Meryem, Elfenni Jamal, Salaheddine Tarik
Radiology Department, Military Hospital Mohammed V, Rabat, Morocco.
Radiol Case Rep. 2023 Jun 1;18(8):2704-2706. doi: 10.1016/j.radcr.2023.04.038. eCollection 2023 Aug.
Bickerstaff brainstem encephalitis (BBE) is a rare inflammatory, demyelinating disease that generally has a good prognosis. It's characterized by an acute dysfunction of brainstem occurring few days after an infection. We report the case of an 11-year-old male child with a history of cold, presented with ataxia in whom a Bickerstaff encephalitis was attested through brain MRI and who has fully recovered after treatment. The main symptoms are ataxia, ophthalmoplegia, and altered consciousness. CSF analysis and serum antiganglioside antibodies are also very suggestive of the diagnosis that can be suspected clinically and confirmed on brain MRI. The interest of this observation lies in its rarity and on the rapid and spectacular clinical improvement under treatment.
比克斯特费尔德脑干脑炎(BBE)是一种罕见的炎症性脱髓鞘疾病,通常预后良好。其特征是在感染后数天出现脑干急性功能障碍。我们报告一例11岁男性儿童病例,该患儿有感冒病史,出现共济失调,经脑部MRI证实为比克斯特费尔德脑炎,经治疗后已完全康复。主要症状为共济失调、眼肌麻痹和意识改变。脑脊液分析和血清抗神经节苷脂抗体也非常有助于临床疑似诊断,并可通过脑部MRI确诊。该病例的意义在于其罕见性以及治疗后临床迅速且显著的改善。